Ganglioneuroma coexisted with renal dysplasia, hydronephrosis and cryptorchidism

We report an unusual case with synchronous occurrence of ganglioneuroma (GN) and multiple urogenital malformations (including ipsilateral renal dysplasia, cryptorchidism and contralateral congenital hydronephrosis). The lesions may be a syndrome associated with embryogenetic disorders. Imaging examinations are helpful for preoperative diagnosis and choose of surgical approach. Staging surgical interventions which taking emphasis on the resection of the tumor was recommended for this case and postoperative histological confirmation, anticipation of malignant transformation of the tumor is also important to ensure a final cure. GN coexisting with multiple urogenital malformations is extremely rare and there is no previous similar reported case.